Cherubism is a rare genetic condition that affects the bones of your lower jaw and sometimes upper jaw. The submandibular and cervical lymph nodes are involved in the early stage.

Both of the greater wings of the sphenoid bones were displaced totally with no involvement of the lateral sphenoid, zygoma, and zygomatic arch. The patient presented to the Maxillofacial Department, Nasser Institute of Health (NIH), for the first time at 2 years of age complaining of mild bilateral swelling in the maxilla and mandible.

Interestingly, after puberty most of the cases regress spontaneously.

Cherubism is a rare childhood fibro-osseous inherited condition, which affects the mandible and maxillary facial bones. Wolters Kluwer Health, Inc. All rights reserved.

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Three-dimensional multislice computed tomography of the maxillofacial bone regions shown in Fig.

In this report we describe the clinical features of a 14-yaer-old girl with a severe case of cherubism affecting both her jaws and we summerize the natural history of the disease over a period of 11 years. Jafarov et al. Severe orbital involvement calls for optic nerve monitoring, which may lead to earlier bony surgical intervention.

In early radiographic images, the angle of the mandible is the first to be affected with multilocular radiolucent changes that are asymptomatic, but can affect the development or eruption of permanent molars.

The name of the disorder is derived from the fact that the chubby-cheeked appearance of the patients resembles the putti, frequently confused with the cherubs, represented in …

The most common mode of inheritance for Cherubism is autosomal dominant with variable penetrance and expressivity.

De Lange J, van den Akker HP, Scholtemeijer M. Jafarov T, Ferimazova N, Reichenberger E. Mangion J, Rahman N, Edkins S, Barfoot R, Nguyen T, Sigurdsson A, et al. The patient with cherubism should have thorough clinical genetic evaluation to rule out the diagnosis of cherubism associated with the Noonan-like syndrome. Cherubism is a rare congenital disease resulting in malformation of the jaw.

As the disease progresses fibrous tissues can invade the floor of the orbits, which cause upward tilting and displacement of the eyes.

A few reports showed no apparent familial involvement.

It can result into enlargement of the jaw bone, tooth displacement, facial disfigurement and psychological trauma to patient.

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